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MedNext Journal of Medical and Health Sciences
Case Report
DOI: 10.54448/mdnt22406
Submitted: 28-10-2022
Published: 28-10-2022

Total collectomy in adult woman with Hirschsprung's Disease: a case report

FAMECA - Faculty of Medicine of Catanduva/Centro Universitário Padre Albino (UNIFIPA), Catanduva, São Paulo, Brazil
FAMECA - Faculty of Medicine of Catanduva/Centro Universitário Padre Albino (UNIFIPA), Catanduva, São Paulo, Brazil
General Surgery, Hospital São Domingos, Catanduva, São Paulo, Brazil
General Surgery at Hospital Padre Albino, Catanduva, São Paulo, Brazil
Centro Universitário Barão de Mauá, Medicine Course, Ribeirão Preto, São Paulo, Brazil
General Surgery at Hospital Padre Albino, Catanduva, São Paulo, Brazil
Faculdade de Medicina de Jundiaí, Faculty of Medicine, Jundiaí, São Paulo, Brazil
General Surgery, Hospital São Domingos, Catanduva, São Paulo, Brazil
FAMECA - Faculty of Medicine of Catanduva/Centro Universitário Padre Albino (UNIFIPA), Catanduva, São Paulo, Brazil
FAMECA - Faculty of Medicine of Catanduva/Centro Universitário Padre Albino (UNIFIPA), Catanduva, São Paulo, Brazil
General Surgery at Hospital Padre Albino, Catanduva, São Paulo, Brazil
FAMECA - Faculty of Medicine of Catanduva/Centro Universitário Padre Albino (UNIFIPA), Catanduva, São Paulo, Brazil
Hirschsprung's disease Congenital megacolon Obstruction

Abstract

Hirschsprung's disease (HD) is a congenital anomaly of innervation of the lower intestine, limited to the colon, resulting from partial or total obstruction. The main symptom is the inability of a newborn to evacuate within 48 hours after birth, which can cause intestinal obstruction in the neonate and megacolon in children and adults. Therefore, this study reported the case of a 30-year-old female patient with HD affecting the entire colon, where we opted for surgical treatment. In the present study, it was emphasized the medical need to have a better understanding of the clinical picture of HD, as well as its complications and the importance of early diagnosis. In the report presented, it was discussed a late diagnosis of HD and how it affects the patient's life. It presented the improvement in the quality of life that can be obtained by offering an accurate diagnosis and adequate treatment for the patient.

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How to Cite

Michelini, B. B., Ferro, C. A., Carvalho, E. P. de, Cadamuro, F. M., Cadamuro, L. M., Criscuolo Filho, L. F., Vivi, M. C. F., Oliveira, M. S. P. de, Miranda, R. M., Silva, T. A. B., Rodrigues, T. F., & Vivi, A. A. G. (2022). Total collectomy in adult woman with Hirschsprung’s Disease: a case report. MedNEXT Journal of Medical and Health Sciences, 3(4). https://doi.org/10.54448/mdnt22406